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Aneurysmal bone cyst (ABC) is a locally aggressive, benign bone tumor that commonly affects children. Metachronous ABCs are rare, and have been described only three times in the literature. Here we present a fourth case in a 9-year-old boy who presented with an ABC of the scapula; 2½ years later he presented with a tibial ABC. We also review the literature and discuss the pathological and clinical characteristics of this lesion.

Intracortical osteosarcoma is the rarest type of osteosarcoma. In most instances the tumor arises in the cortex of the femur, less commonly, in the tibia. We describe an 11-year-old patient with intracortical osteosarcoma of the tibia in whom the tumor was present for 2 years and became painful 3 months prior to presentation.

Hereditary bone dysplasia (HBD) is an extremely rare clinicopathological entity manifested by diaphyseal medullary stenosis and cortical bone thickening associated with a propensity for fractures affecting the long tubular bone. Malignant transformation has been reported to occur at an alarming frequency. The hereditary pattern appears to be autosomal dominant. In this paper we present the case of a 19-year-old man with hereditary bone dysplasia who was unaware of his underlying condition until he presented with malignant transformation arising in an area of bone infarct of the left tibia.

A case of juxtacortical chondromyxoid fibroma in a 31-year-old man was reported. Proof of the diagnosis was obtained by an open biopsy. The histopathology of chondromyxoid fibroma was discussed at length. The radiographic appearances and the differential diagnosis were also described.

An exceptionally rare case of periosteal Ewing's sarcoma involving the mid shaft of the right tibia was reported. In this case, MRI was the technique that confirmed the integrity of the bone marrow. The clinical, radiographic, and histopathologic features of Ewing's sarcoma have been discussed, as has the differential diagnosis of the periosteal type of this tumor.

The overall spectrum of hemangiomas involving long tubular bones is exemplified by three cases, the first being medullary, the second periosteal, and the third intracortical. The clinical presentation was progressive pain at the site of the lesion in all cases. The medullary hemangioma involved the distal shaft of the humerus and was entirely radiolucent. The periosteal tumor was exceptional in that it affected the proximal shaft of the tibia in contrast to the seven previously reported cases that involved the midshaft of the bone. The intracortical hemangioma was in the tibia, the site of all three previously reported cases. Hemangioma of bone may show variable roentgenographic patterns related to the anatomic location and the type of involved bone. The final diagnosis is dependent on histologic evaluation.

We report two cases of fibromyxoma, one affecting the iliac crest and the second involving the proximal shaft of the tibia. Fibromyxoma is a rare neoplasm related to benign fibrous tumors and is characterized by exuberant, extracellular, ground substance production. Its histologic appearance is benign and distinctive and can be readily distinguished from that of myxoid chondrosarcoma or chondromyxoid fibroma. The radiographic picture is, however, difficult to interpret, and the entity can be easily mistaken for other tumors.