1. Acquired Gaucher's cells in Hodgkin's disease
- Author
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Fakhiuddin Ahmed, G. Gomez-Leon, Kyung Shik Lee, Mark S. Tobin, and Karl T.K. Chen
- Subjects
Adult ,Male ,congenital, hereditary, and neonatal diseases and abnormalities ,Pathology ,medicine.medical_specialty ,medicine.medical_treatment ,Disease ,immune system diseases ,Bone Marrow ,hemic and lymphatic diseases ,medicine ,Leukocytes ,Humans ,Aged ,Hodgkin s ,Chemotherapy ,Gaucher Disease ,business.industry ,Complete remission ,nutritional and metabolic diseases ,General Medicine ,Middle Aged ,Hodgkin Disease ,nervous system diseases ,medicine.anatomical_structure ,Glucosylceramidase ,Female ,Bone marrow ,Lymph ,Lymph Nodes ,business ,Glucocerebrosidase ,Glucosidases - Abstract
A patient with Hodgkin's disease associated with low glucocerebrosidase levels in the peripheral leukocytes, and Gaucher's cells in the bone marrow and lymph nodes, is described. After MOPP therapy, complete remission of Hodgkin's disease was accompanied by normalization of the glucocerebrosidase level and disappearance of Gaucher's cells. This observation appears unique when compared with the four cases of combined Hodgkin's and Gaucher's disease reported in earlier literature in which Gaucher's disease remained unchanged after chemotherapy. We conclude that our patient had Hodgkin's disease and acquired Gaucher's cells with diminished glucocerebrosidase levels, rather than a combination of Hodgkin's disease and Gaucher's disease.
- Published
- 1982