Giant ovarian fibrosarcoma: A rare case report

Sex cord–stromal tumors are very rare ovarian tumors. Primary ovarian fibrosarcomas are a very rare type of sex cord–stromal tumors. They arise from superficial or deep connective tissues of fascia, tendon, periosteum, and scar. They can grow either slowly or rapidly forming a giant abdominal mass similar to epithelial tumors of the ovary. Fibrosarcomas are difficult to diagnose preoperatively. Tumor marker and radiological techniques play a trivial role in preoperative diagnosis of this rare variety of sex cord–stromal tumor. Often final diagnosis is made on histopathological and immunohistochemistry reporting. Histopathological features such as high mitotic count, nuclear atypia, and herringbone pattern arrangement of spindle cells confirm a diagnosis of malignant fibrosarcoma. Ki-67 index is considered a prognostic factor for fibromatous lesions of the ovary showing aggressive nature of tumor. We report a rare case of giant ovarian fibrosarcoma in a 40-year-old woman whose diagnosis was made histopathologically due to rarity of tumor.