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Reducing sarcolipin expression mitigates Duchenne muscular dystrophy and associated cardiomyopathy in mice

Authors :
Antanina Voit
Vishwendra Patel
Ronald Pachon
Vikas Shah
Mohammad Bakhutma
Erik Kohlbrenner
Joseph J. McArdle
Louis J. Dell’Italia
Jerry R. Mendell
Lai-Hua Xie
Roger J. Hajjar
Dongsheng Duan
Diego Fraidenraich
Gopal J. Babu
Source :
Nature Communications, Vol 8, Iss 1, Pp 1-14 (2017)
Publication Year :
2017
Publisher :
Nature Portfolio, 2017.

Abstract

Sarcolipin is an inhibitor of the ATP dependent calcium pump SERCA, and is abnormally elevated in Duchenne muscular dystrophy. The authors show that reducing sarcolipin expression ameliorates skeletal muscle pathology and cardiomyopathy and extends life span in mouse models of DMD.

Subjects

Subjects :
Science

Details

Language :
English
ISSN :
20411723
Volume :
8
Issue :
1
Database :
Directory of Open Access Journals
Journal :
Nature Communications
Publication Type :
Academic Journal
Accession number :
edsdoj.201501e20c1241caab7a1010c329171a
Document Type :
article
Full Text :
https://doi.org/10.1038/s41467-017-01146-7