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VCP recruitment to mitochondria causes mitophagy impairment and neurodegeneration in models of Huntington’s disease

Authors :
Xing Guo
XiaoYan Sun
Di Hu
Ya-Juan Wang
Hisashi Fujioka
Rajan Vyas
Sudha Chakrapani
Amit Umesh Joshi
Yu Luo
Daria Mochly-Rosen
Xin Qi
Source :
Nature Communications, Vol 7, Iss 1, Pp 1-17 (2016)
Publication Year :
2016
Publisher :
Nature Portfolio, 2016.

Abstract

Mitochondria defects caused by mutant huntingtin (mtHtt) have been implicated in Huntington's disease. Here authors show that VCP binds to mtHtt on the mitochondria, and that treatment with a peptide that disrupts this interaction reduces the cellular and behavioural deficits in mouse models of HD.

Subjects

Subjects :
Science

Details

Language :
English
ISSN :
20411723
Volume :
7
Issue :
1
Database :
Directory of Open Access Journals
Journal :
Nature Communications
Publication Type :
Academic Journal
Accession number :
edsdoj.1f55ff619f9e46718fcb0202f07879be
Document Type :
article
Full Text :
https://doi.org/10.1038/ncomms12646