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Abnormal Auditory Brainstem Response (ABR) Findings in a Near-Normal Hearing Child with Noonan Syndrome

Authors :
Bahram Jalaei
Mohd Normani Zakaria
Dinsuhaimi Sidek
Source :
Iranian Journal of Otorhinolaryngology, Vol 29, Iss 1, Pp 53-57 (2017)
Publication Year :
2017
Publisher :
Mashhad University of Medical Sciences, 2017.

Abstract

Introduction: Noonan syndrome (NS) is a heterogeneous genetic disease that affects many parts of the body. It was named after Dr. Jacqueline Anne Noonan, a paediatric cardiologist.Case Report: We report audiological tests and auditory brainstem response (ABR) findings in a 5-year old Malay boy with NS. Despite showing the marked signs of NS, the child could only produce a few meaningful words. Audiological tests found him to have bilateral mild conductive hearing loss at low frequencies. In ABR testing, despite having good waveform morphology, the results were atypical. Absolute latency of wave V was normal but interpeak latencies of wave’s I-V, I-II, II-III were prolonged. Interestingly, interpeak latency of waves III-V was abnormally shorter.Conclusion:Abnormal ABR results are possibly due to abnormal anatomical condition of brainstem and might contribute to speech delay.

Details

Language :
English
ISSN :
22517251 and 2251726X
Volume :
29
Issue :
1
Database :
Directory of Open Access Journals
Journal :
Iranian Journal of Otorhinolaryngology
Publication Type :
Academic Journal
Accession number :
edsdoj.1b5bba286f764222a5f297021501f2c0
Document Type :
article
Full Text :
https://doi.org/10.22038/ijorl.2016.8043