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Benefits of pulmonary rehabilitation in patients with advanced lymphangioleiomyomatosis (LAM) compared with COPD – a retrospective analysis

Authors :
Rainer Gloeckl
Christoph Nell
Tessa Schneeberger
Inga Jarosch
Martina Boensch
Henrik Watz
Hubert Wirtz
Tobias Welte
Klaus Kenn
Andreas Rembert Koczulla
Source :
Orphanet Journal of Rare Diseases, Vol 15, Iss 1, Pp 1-4 (2020)
Publication Year :
2020
Publisher :
BMC, 2020.

Abstract

Abstract Lymphangioleiomyomatosis (LAM) is a rare and progressive cystic lung disease with limited therapeutic options. We retrospectively analyzed the effects of a comprehensive 4-week inpatient pulmonary rehabilitation (PR) program in 58 patients with advanced LAM (FEV1: 45 ± 34%predicted, 6-min walk distance (6MWD): 338 ± 167 m). Exercise performance (6MWD: + 49 ± 50 m; p

Details

Language :
English
ISSN :
17501172
Volume :
15
Issue :
1
Database :
Directory of Open Access Journals
Journal :
Orphanet Journal of Rare Diseases
Publication Type :
Academic Journal
Accession number :
edsdoj.0ef9385ea47f4316a138ebcd1ad29a16
Document Type :
article
Full Text :
https://doi.org/10.1186/s13023-020-01540-3