Juvenile Paget's Disease with Paranasal Sinus Aplasia

Authors :: Ki Beom Bae
Jae Hwan Kwon
Young Ho Kim
Tae Young Jung
Joong Hwan Cho
Source :: Clinical and Experimental Otorhinolaryngology, Vol 1, Iss 4, Pp 224-226 (2008)
Publication Year :: 2008
Publisher :: Korean Society of Otorhinolaryngology-Head and Neck Surgery, 2008.
Abstract: Juvenile Paget's disease (JPD) is a rare skeletal disorder that's characterized by bone demineralization and elevated levels of serum alkaline phosphatase. JPD involves the paranasal sinuses in extremely rare cases. We report here on a 25-month-old Asian male who was diagnosed of JPD associated with aplasia of the paranasal sinuses, but not the ethmoid sinuses. The patient was successfully treated by surgery and we undertook no medical intervention. This appears to be the first reported case of JPD associated with bilateral paranasal sinus aplasia.