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Anesthetic management of a child with congenital insensitivity to pain with anhidrosis: A case report

Authors :
Ying Zhang
Zhiyu Geng
Source :
Frontiers in Surgery, Vol 9 (2022)
Publication Year :
2022
Publisher :
Frontiers Media S.A., 2022.

Abstract

Congenital insensitivity to pain with anhidrosis (CIPA) is a rare, autosomal recessive disease classified as hereditary sensory and autonomic neuropathy type VI. Patients with CIPA are characterized by insensitivity to pain, episodes of unexplained fever, anhidrosis, self-mutilating behavior, intellectual disability, and autonomic nervous system abnormalities. The clinical features may intrinsically pose anesthetic challenges. We present a case of a patient with CIPA who underwent tumor biopsy under general anesthesia using a Supreme laryngeal mask airway without any complications. The anesthetic management of this condition is discussed.

Details

Language :
English
ISSN :
2296875X
Volume :
9
Database :
Directory of Open Access Journals
Journal :
Frontiers in Surgery
Publication Type :
Academic Journal
Accession number :
edsdoj.0a8d6c92e834b9eb1e6c6212c9426e4
Document Type :
article
Full Text :
https://doi.org/10.3389/fsurg.2022.997162