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Anesthesia and pain management of a patient with Kleefstra Syndrome for robotic ureteral reimplantation.

Authors :
E. D. Van Der Zwaag
N. A. Bohannon
S. L. Thompson
J. K. Goeller
Source :
Pediatric Anesthesia and Critical Care Journal (PACCJ), Vol 11, Iss 2, Pp 95-99 (2023)
Publication Year :
2023
Publisher :
Pediatric Anesthesia and Critical Care Journal, 2023.

Abstract

Kleefstra syndrome (KS) is a genetic disorder caused by a microdeletion in the 9q34.3 chromosome with related clinical conditions requiring surgical intervention and careful consideration for anesthetic management includ- ing potential difficult airway, cardiac and neurological considerations, pulmonary infections, reflux and delayed gastric emptying, genitourinary abnormalities, hypoto- nia, and seizure disorders. In addition, we observed unique perioperative pain control considerations. We pre- sent a clinical case involving a 2-year-old female who re- ceived anesthesia for robotic ureteral reimplantation sur- gery. Perioperative implications are discussed and con- siderations for anesthetic care provided.

Details

Language :
English
ISSN :
22818421
Volume :
11
Issue :
2
Database :
Directory of Open Access Journals
Journal :
Pediatric Anesthesia and Critical Care Journal (PACCJ)
Publication Type :
Academic Journal
Accession number :
edsdoj.01624a27531e4d09b4e8d6e12d55ca9f
Document Type :
article
Full Text :
https://doi.org/10.14587/paccj.2023.12