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[Buschke's scleredema successfully treated with extracorporeal photopheresis]
- Source :
- La Revue de medecine interne. 39(5)
- Publication Year :
- 2017
-
Abstract
- Scleredema adultorum (Buschke's scleredema) is a cutaneous mucinosis of unknown origin, clinically characterized by a diffuse induration of the skin usually involving the neck, shoulders and back, which limits patients' mobility.We report a case of a 50-year-old woman who presented a chronic sclerodermiform syndrome for 2 years associated with type 1 diabetes. Physical examination revealed an extensive skin induration involving the shoulders, neck and back. Histologic examination confirmed the diagnosis of scleredema adultorum. The patient was treated with extracorporeal photopheresis (EPP) twice a month for two months. At follow-up, mobility was highly improved after two months. Beneficial effect of EPP was maintained on the long term while sessions were spaced.EPP is an unconventional treatment of Buschke's scleredema. We described a case of Buschke's scleredema successfully treated with EPP which may represent a therapeutic option for the treatment of scleredema.
- Subjects :
- Scleredema Adultorum
Photopheresis
Humans
Female
Middle Aged
Skin
Subjects
Details
- Language :
- French
- ISSN :
- 17683122
- Volume :
- 39
- Issue :
- 5
- Database :
- OpenAIRE
- Journal :
- La Revue de medecine interne
- Accession number :
- edsair.pmid..........db1a0889c086a9720778340a056750f0