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Successful surgical repair of pentalogy of cantrell at 14 months of age
- Source :
- Journal of the College of Physicians and Surgeons--Pakistan : JCPSP. 24
- Publication Year :
- 2012
-
Abstract
- Pentalogy of Cantrell with ectopia cordis is a rare congenital anomaly, first described in 1958 by Cantrell, has a reported incidence of around 5-10 cases per one million live births with wide variety of clinical presentations. We are reporting a child with ectopia cordis along with cleft lower sternum, upper abdominal wall defect, ectopic umbilicus and diaphragmatic defect. Echocardiography in first month of life revealed a restrictive perimembranous ventricular septal defect and a small patent Foramen Ovale, both closed spontaneously in infancy. CT angiography at 10 months of age revealed a defect in the thoracic and abdominal walls along with herniation of left ventricular apex into epigastrium. The two ventriculi formed a tail that looked like a crocodile. This patient underwent surgical correction at our institution at 14 months of age and recovered well with no residual issue.
Details
- ISSN :
- 16817168
- Volume :
- 24
- Database :
- OpenAIRE
- Journal :
- Journal of the College of Physicians and Surgeons--Pakistan : JCPSP
- Accession number :
- edsair.pmid..........6d275826a7a847fcd81b164bfd794a67