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[Wyburn-Mason syndrome]
- Source :
- Klinische Monatsblatter fur Augenheilkunde. 208(2)
- Publication Year :
- 1996
-
Abstract
- There are various malformations of retinal vessels. Some of them are associated with cerebral vascular anomalies.This report is given on a girl 6 years of age with a retinal racemose angioma.The clinical examination showed a unilateral racemose angioma combined with retinachorioidal anastomosis and a hemifacial vascular malformation. We found teleangiectasia in this area. The ophthalmoscopy demonstrated a blurred border of optic disc on the right eye with forward protrusion of the disc about + 2.0 dioptres. Large racemose lesions may be localized to the optic nerve and may involve segmental areas of the macula. The ultrasound showed a papillary stasis with highly reflective structures. The ultrasonic patterns are interpreted as a cholesterosis or fibrovascular tissue. This findings may belong to the rare Wyburn-Mason syndrome. Acute neurological symptoms by similar lesions the midbrain and hemorrhages during extraction of teeth are reported in literature.
Details
- Language :
- German
- ISSN :
- 00232165
- Volume :
- 208
- Issue :
- 2
- Database :
- OpenAIRE
- Journal :
- Klinische Monatsblatter fur Augenheilkunde
- Accession number :
- edsair.pmid..........2c6a7899f64b7ef3da99d6735e2f512f