AIRWAY MANAGEMENT IN A CHILD WITH EDWARD’S SYNDROME

Prikazujemo zbrinjavanje dišnog puta u djevojčice s mozaičnim tipom Edwardsovog sindroma za planirani zahvat laparotomije u općoj anesteziji. Manifestacije Edwardsovog sindroma među ostalima su kraniofacijalne malformacije te je moguća otežana ventilacija i intubacija. U našem slučaju djevojčica je, ovisno o potrebi zahvata, imala postavljeno supraglotično pomagalo tijekom anestezije za dijagnostičku pretragu magnetskom rezonancijom (MR), intubirana je fi berbronhoskopski za elektivni zahvat laparoskopije, a u jedinici intenzivne medicine direktnom laringoskopijom. Ventilacija i intubacija protekle su bez komplikacija. Poslijeoperacijski oporavak komplicirao se hipotonijom, pneumonijom te potrebom za reintubacijom i mehaničkom ventilacijom.
We report on airway management in a girl with mosaic type of Edward’s syndrome for elective surgery, laparotomy in general anesthesia. In Edward’s syndrome, among other manifestations, craniofacial anomalies are expressed and there is a possibility of diffi cult ventilation and intubation. In this case, we secured the airway with supraglottic airway device during diagnostics (anesthesia for magnetic resonance imaging), we performed fi beroptic intubation for elective laparoscopy, and in the intensive care unit, she was intubated with direct laryngoscopy. Ventilation and intubation were accomplished without problems. Postoperative recovery was complicated with hypotonia, pneumonia and the need of reintubation and mechanical ventilation.