[症例報告]食道閉鎖症術後に診断された先天性食道狭窄症筋線維肥厚型の1例

A 27-month-old girl with type C esophageal atresia underwent primary anastomosis after birth. Her gestational age was 38 weeks 2 days and weight at birth was 2538 g. At the age of 16 months, she experienced vomiting after consuming solid food. Esophagography indicated absence of stenosis at the anastomotic site; however, tapered narrowing of the lower esophagus was detected. A constriction at the esophagus was detected when the patient underwent endoscopic balloon dilatation for esophageal stenosis twice at the ages of 21 and 25 months. Therefore, a diagnosis of congenital esophageal stenosis due to aberrant tracheobronchial remnants was made. At the age of 27 months, the esophagus along with the constriction was resected via left thoracotomy. Pathological examination of the resected specimen indicated fibromuscular thickness in the stenotic lesion. Thereafter, the patient was discharged and her clinical course was uneventful. Two months after the surgery, esophageal stenosis was found to be absent on esophagography. Previous case reports have frequently attributed congenital esophageal stenosis associated with esophageal atresia to aberrant tracheobronchial remnants, necessitating partial resection of the stenosis. Here, we report the case of a patient with congenital esophageal stenosis due to fibromuscular thickness, successfully treated by partial resection of the stenosis.
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