A fatal case of classic Potter's Syndrome

Potter’s sequence is a rare and fatal disease. There are four types of Potter’s Syndrome. Neonates with classical Potter’s sequence are with oligohydramnios and bilateral renal agenesis. They die shortly after birth because of severe respiratory distress due to pulmonary hypoplasia. Babies have typical physical features — Potter’s face, absence of kidneys and skeletal malformations. We report a fatal case of Potter’s sequence with a typical physical appearance. We performed an autopsy after the delivery.