GIST: A propósito de un término confuso y presentación de un caso de tumor del estroma extragastrointestinal

Purpose: GIST is a soft tissue sarcoma with preferential location for the gastrointestinal tract. However, it has been described in extragastrointestinal tissues. The persistence of the denomination may eventually lead to confusion, because the abbreviation refers to the gastrointestinal tract Material and methods: We present the case of a 57 year old man with initial diagnosis of suffering from a "smooth muscle tumor with uncertain malignant potential", based on its retroperitoneal location. After medical examination and c-kit (CD-117) determination, the definitive diagnosis of "stromal tumor of retroperitoneal location" was made. Conclusions: We propose the term "stromal tumor with Cajal's interstitial cells phenotype".