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A new case of idiopathic hemiplegia hemiconvulsion syndrome
- Publication Year :
- 2010
-
Abstract
- We report a new case of infantile idiopathic hemiconvulsion-hemiplegia syndrome (HH). A prolonged right-sided febrile convulsion was followed 4 days later, by right hemiconvulsive status epilepticus, documented by video-electroencephalogram (EEG) recording. The child developed an ipsilateral hemiplegia, partially improved during the first month of follow-up. Sequential cerebral magnetic resonance imaging (MRI) and proton magnetic resonance spectroscopy (1H-MRS) at 6, 15, 30 days of follow-up showed a cytotoxic edema in the left hemisphere and a subsequent necrosis. At 1-year of follow-up, we performed MRI control because of febrile convulsion lasting few minutes that confirmed a non-progressive left hemisphere atrophy. After 2 years, the patient was seizure-free, with a mild right hemiplegia and language skills deficit. We discuss the unclear pathogenesis of HH through sequential neuroradiological evaluation.
- Subjects :
- Male
medicine.medical_specialty
Neurology
Brain Edema
Hemiplegia
Epilepsy, Partial, Motor
Dermatology
Status epilepticus
Seizures, Febrile
Lateralization of brain function
Epilepsy
Atrophy
Convulsion
medicine
Humans
Neuroradiology
medicine.diagnostic_test
business.industry
Infant
Magnetic resonance imaging
Syndrome
General Medicine
medicine.disease
Magnetic Resonance Imaging
Psychiatry and Mental health
Anesthesia
Neurology (clinical)
medicine.symptom
business
Subjects
Details
- Language :
- English
- Database :
- OpenAIRE
- Accession number :
- edsair.doi.dedup.....c46f4e3beed830ae2a55ba69f7971729