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Striking Visualization of Diffuse Congenital Nesidioblastosis on Ga-68 DOTATATE PET/CT
- Source :
- Molecular Imaging and Radionuclide Therapy, Vol 28, Iss 2, Pp 83-85 (2019), Molecular Imaging and Radionuclide Therapy
- Publication Year :
- 2019
- Publisher :
- Galenos Yayinevi, 2019.
-
Abstract
- “Nesidioblastosis”, later renamed as “persistent hyperinsulinemic hypoglycemia of infancy” presents as either focal or diffuse neo-differentiation of pancreatic Langerhans islet cells from the ductal epithelium. Differentiation of focal disease from diffuse involvement is crucial for optimal disease management. The current methods used to differentiate the two forms pre-operatively are invasive techniques. The definite role of imaging modalities to differentiate diffuse versus focal form has not yet been proven. Herein, we report a 15 day-old infant having diffuse nesidioblastosis, successfully demonstrated by Ga-68 DOTATATE positron emission tomography/computed tomography imaging that was histopathologically confirmed.Pankreasın Langerhans ada hücrelerinin duktus epitelinden yeniden farklılaşması olan “nesidioblastosis”, yeni adlandırılmasıyla “yenidoğanın inatçı hiperinsülinemik hipoglisemisi”, fokal ya da diffüz olarak iki şekilde görülebilir. Fokal formun diffüz olandan ayırt edilmesi hastalığın doğru yönetimi için son derece önemlidir. Bu iki formun cerrahi öncesi ayrımında kullanılan güncel metodlar invaziftir. Görüntülemenin diffüz formu fokal olandan ayırt etmedeki rolü tam olarak ortaya konamamıştır. Burada, Ga-68 DOTATATE pozitron emisyon tomografi/bilgisayarlı tomografi görüntüleme ile başarılı bir şekilde gösterilen ve histopatolojik olarak da doğrulanan diffüz nesidioblastosis hastası 15 günlük bir infant olgusunu sunduk.
- Subjects :
- lcsh:Medical physics. Medical radiology. Nuclear medicine
Pathology
medicine.medical_specialty
lcsh:R895-920
Nesidioblastosis
lcsh:Medicine
Computed tomography
medicine.disease_cause
Imaging modalities
Islet cells
differential diagnosis
medicine
Radiology, Nuclear Medicine and imaging
Hyperinsulinemic hypoglycemia
Ga-68 DOTATATE PET/CT
PET-CT
lcsh:R5-920
medicine.diagnostic_test
business.industry
lcsh:R
medicine.disease
Positron emission tomography
Interesting Image
hyperinsulinemic hypoglycemia
Differential diagnosis
business
lcsh:Medicine (General)
Subjects
Details
- Language :
- English
- ISSN :
- 21471959 and 21461414
- Volume :
- 28
- Issue :
- 2
- Database :
- OpenAIRE
- Journal :
- Molecular Imaging and Radionuclide Therapy
- Accession number :
- edsair.doi.dedup.....b75b5b90f77347a0194b7b7d7988f3bc