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Hailey-Hailey disease is caused by mutations in ATP2C1 encoding a novel Ca(2+) pump

Authors :
Carol Dobson-Stone
Jacqueline K. White
Marc Perrussel
Eugene Healy
Tom Strachan
Alain Hovnanian
Juliane Ramser
Anthony P. Monaco
Hans Lehrach
Joanna Brown
Marc Larrègue
Ralf Sudbrak
S. Carter
Colin S. Munro
M.A.K.L. Dissanayake
Susan Burge
Source :
Human molecular genetics. 9(7)
Publication Year :
2000

Abstract

Hailey-Hailey disease (HHD) is an autosomal dominant skin disorder characterized by suprabasal cell separation (acantholysis) of the epidermis. Previous genetic linkage studies localized the gene to a 5 cM interval on human chromosome 3q21. After reducing the disease critical region to

Details

ISSN :
09646906
Volume :
9
Issue :
7
Database :
OpenAIRE
Journal :
Human molecular genetics
Accession number :
edsair.doi.dedup.....b3c32c515fb0d16860b5ff5fbc316a24