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A Rare Case of Kikuchi Fujimoto’s Disease with Subsequent Development of Systemic Lupus Erythematosus

Authors :
Brent Kelly
You Wen Qian
Michelle Foshat
Yu Zuo
Bernard Karnath
Brock Harper
Source :
Case Reports in Rheumatology, Case Reports in Rheumatology, Vol 2012 (2012)
Publication Year :
2012
Publisher :
Hindawi Limited, 2012.

Abstract

Kikuchi Fujimoto’s disease (KFD) is a rare, immune-mediated, self-limiting disorder with unique histopathological features. KFD is usually seen in young Asian females; however, cases have been reported throughout the world and in all ethnicities. It has been recognized that there is a rare association between Systemic Lupus Erythematosus (SLE) and KFD via sporadic case reports. The exact pathophysiological relationship between these two diseases is still unclear. We report a case of a young Asian female who presented with persistent fever and lymphadenopathy and was diagnosed with Kikuchi Fujimoto’s disease based on lymph node biopsy; although an SLE workup was done, she did not meet the American Rheumatology Association (ARA) diagnostic criteria for lupus, and the lymph node biopsy did not show features of SLE. She improved clinically with a short course of steroid therapy. Two months later, the patient presented with central facial rash and arthralgia. SLE workup was repeated, a skin biopsy was done, and the results at this time supported a diagnosis of SLE.

Details

ISSN :
20906897 and 20906889
Volume :
2012
Database :
OpenAIRE
Journal :
Case Reports in Rheumatology
Accession number :
edsair.doi.dedup.....b16f21b9e550c5447c93c55dc32bc6f2
Full Text :
https://doi.org/10.1155/2012/325062