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Thoracic insufficiency syndrome: Approaches to assessment and management
- Source :
- Paediatric Respiratory Reviews. 44:78-84
- Publication Year :
- 2022
- Publisher :
- Elsevier BV, 2022.
-
Abstract
- Thoracic insufficiency syndrome (TIS) was described in 2003 as the inability of the thorax to support normal respiration or lung growth. TIS includes a broad and disparate group of typically degenerative thoracospinal conditions. Although TIS arises due to a heterogeneous group of disorders and thus its incidence is not well quantified, general approaches to management and treatment exist. Evolving imaging techniques and measurements of health-related quality of life augment tests of pulmonary function to quantify disease burden, longitudinally and pre- and post-intervention. Intervention is primarily via growth-sparing surgery, for which several device options exist, to preserve vertical growth prior to a definitive spinal fusion at skeletal maturity.
Details
- ISSN :
- 15260542
- Volume :
- 44
- Database :
- OpenAIRE
- Journal :
- Paediatric Respiratory Reviews
- Accession number :
- edsair.doi.dedup.....a9f99b9585c49cfdac8f5867864880cc