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Case Report: Clinical manifestation and dental management of Papillon-Lefèvre syndrome
- Source :
- F1000Research
- Publication Year :
- 2018
- Publisher :
- F1000 Research Ltd, 2018.
-
Abstract
- Background:Papillon-Lefèvre syndrome (PLS) is considered a rare syndrome, which is characterized by the presence of palmar-plantar hyperkeratosis and aggressively progressing periodontitis that finally leads to premature loss of both deciduous and permanent teeth.Case report:A four-year-old Egyptian boy presented with a maternal complaint that her child suffers from early loss of many teeth, presence of loose teeth along with an asymptomatic swelling related to the upper anterior area. The patient was diagnosed with PLS. A symptomatic management and prevention program was followed and the swelling was excised; afterwards diagnosed as peripheral ossifying fibroma.Conclusion:Early recognition and intervention for patients with PLS is essential to avoid the threat of being edentulous if left unmanaged.
- Subjects :
- Male
0301 basic medicine
medicine.medical_specialty
Hyperkeratosis
Case Report
Papillon–Lefèvre syndrome
Clinical manifestation
Asymptomatic
General Biochemistry, Genetics and Molecular Biology
03 medical and health sciences
Papillon-Lefevre Disease
0302 clinical medicine
Palmoplantar keratosis
medicine
Humans
Rare syndrome
General Pharmacology, Toxicology and Pharmaceutics
Periodontitis
Permanent teeth
Premature tooth loss
General Immunology and Microbiology
business.industry
Peripheral ossifying fibroma
Articles
030206 dentistry
General Medicine
medicine.disease
Dermatology
stomatognathic diseases
030104 developmental biology
Child, Preschool
Papillon – Lefèvre syndrome
Egypt
Mouth, Edentulous
medicine.symptom
business
Subjects
Details
- ISSN :
- 20461402
- Volume :
- 7
- Database :
- OpenAIRE
- Journal :
- F1000Research
- Accession number :
- edsair.doi.dedup.....a8b5828bb62f6633b16599434bf05ec3