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Malignant Peripheral Nerve Sheath Tumor Arising from Small Bowel Mesentery: an Extremely Rare Case with Review of Literature
- Source :
- Journal of gastrointestinal cancer.
- Publication Year :
- 2021
-
Abstract
- PURPOSE Malignant peripheral nerve sheath tumor (MPNST) of small bowel mesentery is a rare tumor. We report a rare case of MPNST of small bowel mesentery in a patient without neurofibromatosis (NF). METHODS A 50-year-old male, with no features suggestive of NF1, presented to us with complaints of pain abdomen. Contrast-enhanced computed tomography (CECT) of the abdomen revealed a mass in the infrarenal region. On laparotomy, mass was seen to be arising from the mesentery of the jejunum. En-bloc resection of the tumor was done, and histopathological examination was suggestive of malignant peripheral nerve sheath tumor of the small bowel mesentery. RESULT Patient received adjuvant external beam radiotherapy to a dose of 50.4 Gy to the tumor bed. The patient was planned for chemotherapy but absconded and later came with recurrence. The patient finally succumbed to disease. CONCLUSION Surgery is the mainstay of treatment. Adjuvant treatment should be based on histopathological report.
- Subjects :
- medicine.medical_specialty
Chemotherapy
business.industry
medicine.medical_treatment
Gastroenterology
Malignant peripheral nerve sheath tumor
medicine.disease
Jejunum
medicine.anatomical_structure
Oncology
Laparotomy
Medicine
Abdomen
External beam radiotherapy
Radiology
Neurofibromatosis
business
Mesentery
Subjects
Details
- ISSN :
- 19416636
- Database :
- OpenAIRE
- Journal :
- Journal of gastrointestinal cancer
- Accession number :
- edsair.doi.dedup.....a6bbc88b1d6f95aab1534cc9bc14b1c6