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Ventricular noncompaction and long QT syndrome – A deadly double hit for the foetus
- Source :
- Indian Pacing and Electrophysiology Journal, Indian Pacing and Electrophysiology Journal, Vol 21, Iss 3, Pp 186-190 (2021)
- Publication Year :
- 2021
- Publisher :
- Elsevier BV, 2021.
-
Abstract
- Congenital long QT syndrome [LQTS] is a channelopathy characterized by QT prolongation and polymorphic VT. LQTS however need not be a purely electrical disease. Defects in ion channels may cause myocardial architectural disruption leading to ventricular non compaction [VNC]. It is defined as the presence of prominent ventricular trabeculations and deep intertrabecular recesses within the endomyocardium. We describe the in-utero management of a foetus who was later found to have LQTS with VNC. The detection of ventricular tachycardia and complete heart block in utero should arouse the suspicion of LQTS. It would be wise to avoid QT prolonging antiarrhythmics in this subset of patients.
- Subjects :
- AV, Atrioventricular
congenital, hereditary, and neonatal diseases and abnormalities
medicine.medical_specialty
Double hit
Heart block
Long QT syndrome
Ventricular non compaction
Case Report
030204 cardiovascular system & hematology
Ventricular tachycardia
Low resource setting
QT interval
03 medical and health sciences
0302 clinical medicine
Channelopathy
Physiology (medical)
Internal medicine
medicine
Diseases of the circulatory (Cardiovascular) system
ICD, Implantable Cardioverter Defibrillator
cardiovascular diseases
030212 general & internal medicine
Fetus
VT, Ventricular tachycardia
business.industry
LQTS, Long QT Syndrome
Fetal arrhythmias
medicine.disease
VNC, Ventricular Non compaction
Electrophysiology
Congenital long QT syndrome
RC666-701
Cardiology
Cardiology and Cardiovascular Medicine
business
Subjects
Details
- ISSN :
- 09726292
- Volume :
- 21
- Database :
- OpenAIRE
- Journal :
- Indian Pacing and Electrophysiology Journal
- Accession number :
- edsair.doi.dedup.....a58c302ef959dad6763d93d3f1a9fa56