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Linear atrophoderma of Moulin: an underrecognized entity
- Source :
- Pediatric Rheumatology Online Journal
- Publication Year :
- 2015
-
Abstract
- Linear atrophoderma of Moulin (LAM) is an acquired skin condition that manifests in early childhood and adolescence. It likely represents a form of cutaneous mosaicism that presents with linear, hyperpigmented and atrophic lesions appearing on the trunk and limbs. Its clinical appearance varies and may closely resemble that of atrophoderma of Pasini and Pierini (APP) and linear scleroderma. LAM usually follows a benign course and no effective treatment options exist. We present a case of a young and healthy patient that developed such lesions on her upper and lower extremities over 5 years. The initial clinical impression of linear scleroderma was reviewed in favor of LAM following histological examination of the lesions which revealed no significant inflammatory changes. LAM remains a rare and possibly under recognized entity with reports confined only to the dermatologic literature. This case highlights the importance of recognizing LAM and distinguishing it from linear scleroderma given the significant differences in management and prognosis.
- Subjects :
- Pathology
medicine.medical_specialty
Adolescent
Case Report
Linear atrophoderma of Moulin
Scleroderma
Diagnosis, Differential
Scleroderma, Localized
Rheumatology
Hyperpigmentation
medicine
Immunology and Allergy
Humans
Linear Scleroderma
Pediatrics, Perinatology, and Child Health
Child
Histological examination
Skin
Atrophoderma of Pasini and Pierini
business.industry
Clinical appearance
medicine.disease
Pediatrics, Perinatology and Child Health
Atrophoderma
Female
Differential diagnosis
medicine.symptom
Atrophy
business
Subjects
Details
- ISSN :
- 15460096
- Volume :
- 13
- Issue :
- 1
- Database :
- OpenAIRE
- Journal :
- Pediatric rheumatology online journal
- Accession number :
- edsair.doi.dedup.....a48b606bf73f96120f6ba7210854f65f