PReS-FINAL-2359: Renal involvement in hypocomplementemic urticarial vasculitis syndrome (huvs): report of 3 paediatric cases

HUVS is a rare disease characterized by persistent urticarial lesions with histological evidence of leucocytoclastic vasculitis and complement activation with a marked decrease in circulating C1q levels. HUVS can present systemic features involving the musculoskeletal, pulmonary, renal and gastrointestinal systems; its peak incidence is in the fifth decade of life. The exact prevalence of HUVS in children is unknown.