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Early onset of cardiomyopathy and primary prevention of sudden death in X-linked Emery-Dreifuss muscular dystrophy
- Source :
- Neuromuscular disorders : NMD. 20(3)
- Publication Year :
- 2008
-
Abstract
- We report the case of 14-year-old boy with X-linked Emery-Dreifuss muscular dystrophy who developed sick sinus syndrome and required placement of an implantable intracardiac cardioverter-defibrillator (ICD) to prevent sudden death. He demonstrated no significant risk factors for sudden death such as depressed left ventricular ejection fraction, or spontaneous or inducible ventricular tachycardia. One month after implantation, the patient experienced one appropriate ICD discharge.
- Subjects :
- Tachycardia
Male
medicine.medical_specialty
Adolescent
medicine.medical_treatment
Cardiomyopathy
Ventricular tachycardia
Sudden death
Sick sinus syndrome
Sudden cardiac death
Electrocardiography
Internal medicine
medicine
Humans
Emery-Dreifuss - ICD implantation
cardiovascular diseases
Muscular dystrophy
Genetics (clinical)
Sick Sinus Syndrome
business.industry
medicine.disease
Implantable cardioverter-defibrillator
Muscular Dystrophy, Emery-Dreifuss
Defibrillators, Implantable
Death, Sudden, Cardiac
Neurology
Pediatrics, Perinatology and Child Health
cardiovascular system
Cardiology
Tachycardia, Ventricular
Neurology (clinical)
medicine.symptom
business
Cardiomyopathies
Subjects
Details
- ISSN :
- 18732364
- Volume :
- 20
- Issue :
- 3
- Database :
- OpenAIRE
- Journal :
- Neuromuscular disorders : NMD
- Accession number :
- edsair.doi.dedup.....9f0d362d6b1fda421cbf4239f3c7b026