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INVERSE KLIPPEL-TRENAUNAY SYNDROME
- Source :
- Revista Paulista de Pediatria, Vol 38 (2020), Revista Paulista de Pediatria
- Publication Year :
- 2020
- Publisher :
- Sociedade de Pediatria de São Paulo, 2020.
-
Abstract
- Objective: To report a rare case of inverse Kipplel-Trenaunay. Case description: A 16-year-old girl with a grayish-depressed plaque on her left thigh. Angioresonance showed a vascular malformation affecting the skin and subcutaneous tissue. Comments: Inverse Klippel-Trenaunay is a Klippel-Trenaunay syndrome variation in which there are capillary and venous malformations associated to hypotrophy or shortening of the affected limb. Modifications on the limb’s length or width result from alterations in bones, muscles, or subcutaneous tissues. It has few described cases. Further clinical and molecular studies must be performed for a proper understanding.
- Subjects :
- Klippel-Trenaunay syndrome
030309 nutrition & dietetics
Síndrome de Klippel-Trenaunay-Weber
Klippel-Trenaunay-Weber syndrome
Case Report
Pediatrics
RJ1-570
03 medical and health sciences
0302 clinical medicine
Tela subcutânea
030225 pediatrics
Rare case
medicine
Subcutaneous tissue
Vascular diseases
Anormalidades da pele
0303 health sciences
business.industry
Vascular malformation
Left thigh
Skin abnormality
Anatomy
Doenças vasculares
Case description
medicine.disease
medicine.anatomical_structure
Skin abnormalities
Pediatrics, Perinatology and Child Health
Klippel-Trenaunay-Weber Syndrome
business
Subjects
Details
- Language :
- English
- ISSN :
- 19840462
- Volume :
- 38
- Database :
- OpenAIRE
- Journal :
- Revista Paulista de Pediatria
- Accession number :
- edsair.doi.dedup.....9c553551bb7a814b6350807af5103cc4