Bilateral exudative retinal detachments in Sturge-Weber syndrome

An 11-year-old girl with a port-wine stain on both sides of her face (fi gure A, B) presented after reporting progressive diffi culty reading. Visual acuity in the right eye was 20/100 and in the left eye she could count fi ngers only. Fundus examination of the right eye showed an inferior retinal detachment with retinal pleats (fi gure C, arrow). A subretinal peripapillary lesion was also seen. Dilated examination of the left eye showed a bullous retinal detachment that could be seen through the pupil Lancet 2013; 382: 259