Back to Search Start Over

[A perspective on the control of myositis ossificans progressiva]

Authors :
Ligia Maria Leme
Durval Batista Palhares
Source :
Jornal de pediatria. 77(5)
Publication Year :
2003

Abstract

OBJECTIVE: to report four cases of myositis ossificans progressiva, its form of presentation, in addition to new control and treatment options. DESCRIPTION: the authors describe four cases of myositis ossificans progressiva, presenting its clinical manifestations, evolution, and available forms of control and treatment. The main congenital anomalies associated with myosistis ossificans progressiva are described, namely: hallux valgus, clinodactyly, short thumbs, exostosis, and syndactyly. The evolution and therapeutic responses of clinical improvement to oral ascorbic acid and biphosphonate in patients 1 and 4 are also described; patient 1 had a better response after receiving intravenous biphosphonate, while patients 2 and 3 showed clinical improvement after the administration of oral ascorbic acid. COMMENTS: ascorbic acid relieves the pain and improves psychism in patients with myositis ossificans progressiva. Intravenous biphosphonate is an alternative to patients with significant worsening of the disease, especially those with ambulatory restrictions. The orientation towards avoiding recurrent trauma in myositis ossificans progressiva patients is important.

Details

ISSN :
16784782
Volume :
77
Issue :
5
Database :
OpenAIRE
Journal :
Jornal de pediatria
Accession number :
edsair.doi.dedup.....8705335331572780e80941b537bbb53b