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A group of patients with Marfan's syndrome, who have finger and toe contractures, displays tendons' alterations upon an ultrasound examination: are these features common among classical Marfan patients?
- Source :
- Internal and emergency medicine. 11(5)
- Publication Year :
- 2015
-
Abstract
- The involvement of the musculoskeletal system with other mild pleiotropic manifestations represents a clinical criterion, called "systemic features," to d iagnose Marfan's syndrome. We aimed to investigate the features of the hands and feet redressable contractures present in a group of Marfan patients. In 13 patients with previously diagnosed Marfan's syndrome, an accurate clinical examination was performed. In particular the characterization of the musculoskeletal system by visual analogic scale to measure muscle pain (VAS) and muscle strength (MRC system) was carried out; the Beighton scale score was used to evaluate the articular hypermobility. Ultrasound examination (US) was performed to detect deep-superficial flexor tendons and extensor tendons of both hands, and the short and long flexor and extensor tendons of the fingers and toes in static and dynamic positions. The ImageJ program was adopted to measure a profile of tendon echo-intensity. A reduction of the thickness of all tendons was detected by US in our patients; the VAS and Beighton scale scores were in normal ranges. The profile of tendon echo-intensity showed different textural details in all Marfan patients. This study provides evidence for other contractures' localization, and for altered findings of the tendons in patients with Marfan syndrome and finger/toe contractures. These changes may be associated with structural modifications in connective tissue.
- Subjects :
- musculoskeletal diseases
0301 basic medicine
Marfan syndrome
Adult
Male
Contracture
medicine.medical_treatment
Connective tissue
Physical examination
Marfan Syndrome
Fingers
Tendons
03 medical and health sciences
0302 clinical medicine
Internal Medicine
medicine
Humans
Reduction (orthopedic surgery)
Muscle contracture
Aged
Pain Measurement
Ultrasonography
medicine.diagnostic_test
business.industry
Ultrasound
Anatomy
Middle Aged
Toes
musculoskeletal system
medicine.disease
Tendon
030104 developmental biology
medicine.anatomical_structure
Emergency Medicine
Female
medicine.symptom
business
030217 neurology & neurosurgery
Subjects
Details
- ISSN :
- 19709366
- Volume :
- 11
- Issue :
- 5
- Database :
- OpenAIRE
- Journal :
- Internal and emergency medicine
- Accession number :
- edsair.doi.dedup.....7e955f857232fe61f39173199bdaf757