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Successful Brace Treatment of Pectus Carinatum in Osteogenesis Imperfecta Using the Dynamic Compression System

Authors :
Uri S. Alon
Beth A. Orrick
Charles L. Snyder
Amy L. Pierce
Source :
European Journal of Pediatric Surgery Reports, European Journal of Pediatric Surgery Reports, Vol 07, Iss 01, Pp e117-e120 (2019)
Publication Year :
2019
Publisher :
Georg Thieme Verlag KG, 2019.

Abstract

Osteogenesis imperfecta (OI) is a genetic disorder of collagen resulting in a “fragile” skeleton with increased fracture risk and other complications, dependent on the specific variant. Pectus deformities of the chest wall, while not common, can be associated with OI. The use of a pectus carinatum brace in a patient with OI poses unknown risks for fractures and adverse treatment outcomes. We successfully applied external compression bracing using the dynamic compression system to one such patient. This case illustrates the ability to treat an OI patient with pectus carinatum using a nonsurgical brace, without complications, resulting in an excellent cosmetic result.

Details

ISSN :
21947627 and 21947619
Database :
OpenAIRE
Journal :
European Journal of Pediatric Surgery Reports
Accession number :
edsair.doi.dedup.....7afd56489eeb03c0c9b154e88879a4ec