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Idiopathic Adulthood Ductopenia Causing Cirrhosis
- Source :
- ACG Case Reports Journal
- Publication Year :
- 2020
- Publisher :
- Wolters Kluwer, 2020.
-
Abstract
- Idiopathic adulthood ductopenia (IAD) is a chronic small duct cholestatic biliary disease that is characterized by the loss of interlobular bile ducts. It is diagnosed when there is biochemical evidence of cholestatic liver disease, ductopenia on liver biopsy, and no other identifiable cause of cholestasis. We present a patient with 10 days of progressive abdominal pain, jaundice, and worsening liver function tests who advanced to fulminant liver failure with no apparent underlying cause. He was found to have cirrhosis, with biopsy demonstrative of ductopenia, consistent with idiopathic adulthood ductopenia, which is a rare etiology of cirrhosis but should be considered when the typical workup yields no answer.
- Subjects :
- medicine.medical_specialty
Cirrhosis
medicine.diagnostic_test
business.industry
Case Report
General Medicine
Jaundice
medicine.disease
Gastroenterology
Biliary disease
Interlobular bile ducts
03 medical and health sciences
0302 clinical medicine
Ductopenia
Cholestasis
Liver
030220 oncology & carcinogenesis
Liver biopsy
Internal medicine
medicine
030211 gastroenterology & hepatology
medicine.symptom
Liver function tests
business
Subjects
Details
- Language :
- English
- ISSN :
- 23263253
- Volume :
- 7
- Issue :
- 3
- Database :
- OpenAIRE
- Journal :
- ACG Case Reports Journal
- Accession number :
- edsair.doi.dedup.....687d386f19b96eade77382f6c65f3e6d