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Specific muscle strength is reduced in facioscapulohumeral dystrophy: An MRI based musculoskeletal analysis
- Source :
- Neuromuscular Disorders, 28, 3, pp. 238-245, Neuromuscular disorders, 28(3), 238-245. Elsevier, Neuromuscular Disorders, 28, 238-245
- Publication Year :
- 2018
-
Abstract
- Item does not contain fulltext The aim was to test whether strength per unit of muscle area (specific muscle strength) is affected in facioscapulohumeral dystrophy (FSHD) patients, as compared to healthy controls. Ten patients and ten healthy volunteers underwent an MRI examination and maximum voluntary isometric contraction measurements (MVICs) of the quadriceps muscles. Contractile muscle volume, as obtained from the MR images, was combined with the MVICs to calculate the physiological cross-sectional area (PCSA) and muscle strength using a musculoskeletal model. Subsequently, specific strength was calculated for each subject as muscle strength divided by total PCSA. FSHD patients had a reduced quadriceps muscle strength (median(1st quartile-3rd quartile): 2011 (905.4-2775) N vs. 5510 (4727-8321) N, p
- Subjects :
- Adult
Male
0301 basic medicine
Muscle tissue
medicine.medical_specialty
UT-Hybrid-D
Isometric exercise
Specific strength
Young Adult
03 medical and health sciences
0302 clinical medicine
Atrophy
Facioscapulohumeral muscular dystrophy
Isometric Contraction
Internal medicine
Urological cancers Radboud Institute for Molecular Life Sciences [Radboudumc 15]
medicine
Humans
Muscle Strength
Muscle, Skeletal
Genetics (clinical)
Aged
Intrinsic weakness
business.industry
Dystrophy
Quantitative MRI
Middle Aged
medicine.disease
Disorders of movement Donders Center for Medical Neuroscience [Radboudumc 3]
Magnetic Resonance Imaging
Muscular Dystrophy, Facioscapulohumeral
Reconstructive and regenerative medicine Radboud Institute for Health Sciences [Radboudumc 10]
030104 developmental biology
medicine.anatomical_structure
Neurology
Quartile
Pediatrics, Perinatology and Child Health
Musculoskeletal modeling
Cardiology
Muscle strength
Female
Neurology (clinical)
business
030217 neurology & neurosurgery
Subjects
Details
- ISSN :
- 09608966
- Database :
- OpenAIRE
- Journal :
- Neuromuscular Disorders, 28, 3, pp. 238-245, Neuromuscular disorders, 28(3), 238-245. Elsevier, Neuromuscular Disorders, 28, 238-245
- Accession number :
- edsair.doi.dedup.....5d4a4dfaec2281a717c077fc564fc41f