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Primary ovarian high-grade endometrial stromal sarcoma: a case report
- Source :
- Journal of Medical Case Reports, Vol 15, Iss 1, Pp 1-5 (2021), Journal of Medical Case Reports
- Publication Year :
- 2021
- Publisher :
- BMC, 2021.
-
Abstract
- Background Primary ovarian high-grade endometrial stromal sarcoma is a very rare disease. Even though it has poor prognosis, the gold standard treatment has not been established owing to its rarity. This report aimed to present therapeutic options for primary ovarian high-grade endometrial stromal sarcoma. Case presentation A 49-year-old Asian woman presented with disseminated intravascular coagulation due to ruptured primary high-grade ovarian endometrial stromal sarcoma with multiple intraperitoneal metastases. After the initial surgery, the patient underwent adjuvant chemotherapy with three courses of Adriamycin (75 mg/m2). We performed the secondary debulking operation including total hysterectomy, metastasectomy, omentectomy, peritonectomy, appendectomy, and hyperthermic intraperitoneal chemotherapy (paclitaxel 175 mg/m2). Currently she has been alive for 28 months under a new chemotherapy regimen. Conclusion We suggest cytoreductive surgery with hyperthermic intraperitoneal chemotherapy could be a therapeutic option for primary high-grade ovarian endometrial stromal sarcoma with peritoneal dissemination.
- Subjects :
- 0301 basic medicine
Oncology
Poor prognosis
medicine.medical_specialty
Sarcoma, Endometrial Stromal
Case Report
Hysterectomy
Primary ovarian high-grade endometrial stromal sarcoma
03 medical and health sciences
0302 clinical medicine
Surgical oncology
Internal medicine
medicine
Humans
Endometrial stromal sarcoma
HIPEC
business.industry
Ovary
Gold standard
General Medicine
Middle Aged
medicine.disease
Endometrial Neoplasms
030104 developmental biology
Chemotherapy, Adjuvant
030220 oncology & carcinogenesis
Medicine
Female
business
Rare disease
Subjects
Details
- Language :
- English
- ISSN :
- 17521947
- Volume :
- 15
- Issue :
- 1
- Database :
- OpenAIRE
- Journal :
- Journal of Medical Case Reports
- Accession number :
- edsair.doi.dedup.....4a5ecf164531813c004e9d446d532966