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Beating the odds: a rare case of supracardiac total anomalous pulmonary venous return (TAPVR) in an adult patient

Authors :
Norain Talib
Mohd Rizal Mohd Zain
Mohd Shafie Abdullah
Khairil Amir Sayuti
Source :
BMJ case reports. 2018
Publication Year :
2018

Abstract

Total anomalous pulmonary venous return (TAPVR) is a rare congenital heart defect, and patients are usually symptomatic at a very young age. Survival to adulthood without surgical correction is extremely rare. We report a 33-year-old woman with a heart murmur and a history of a successful pregnancy. Echocardiogram revealed a large atrial septal defect with suspicious pulmonary vein anomaly. Chest radiograph demonstrated classical 'snowman' configuration. Cardiac catheterisation was consistent with anomalous pulmonary venous drainage. Cardiac CT confirmed supracardiac TAPVR, whereby all the pulmonary veins drain into the anomalous vein and finally to the superior vena cava. She remained asymptomatic and underwent a successful surgical repair.

Details

ISSN :
1757790X
Volume :
2018
Database :
OpenAIRE
Journal :
BMJ case reports
Accession number :
edsair.doi.dedup.....28612792fc5f4aac3a0f3d167c23b1a7