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<html>Prognostic impact of c-Rel nuclear expression and REL amplification and crosstalk between c-Rel and the p53 pathway in diffuse large B-cell lymphoma</html>

Authors :
Young, Ken H.
Piris, Miguel A.
Ferreri, Andrés J.M.
van Krieken, J. Han
Huh, Jooryung
Ponzoni, Maurilio
Xu-Monette, Zijun Y.
Zu, Youli
Hsi, Eric D.
Richards, Kristy L.
Jeffrey Medeiros, L.
Møller, Michael B.
Ok, Chi Young
Montes-Moreno, Santiago
Manyam, Ganiraju C.
Chiu, April
Dybkaer, Karen
Tzankov, Alexandar
Wang, Jinfen
Parsons, Ben M.
Visco, Carlo
Choi, William W.L.
Winter, Jane N.
Li, Ling
Pham, Lan V.
Zhang, Mingzhi
Sun, Ruifang
Orazi, Attilio
Bhagat, Govind
Publication Year :
2015
Publisher :
The University of North Carolina at Chapel Hill University Libraries, 2015.

Abstract

Dysregulated NF-κB signaling is critical for lymphomagenesis. The regulation, function, and clinical relevance of c-Rel/NF-κB activation in diffuse large B-cell lymphoma (DLBCL) have not been well studied. In this study we analyzed the prognostic significance and gene-expression signature of c-Rel nuclear expression as surrogate of c-Rel activation in 460 patients with de novo DLBCL. Nuclear c-Rel expression, observed in 137 (26.3%) DLBCL patients frequently associated with extranoal origin, did not show significantly prognostic impact in the overall- or germinal center B-like-DLBCL cohort, likely due to decreased pAKT and Myc levels, up-regulation of FOXP3, FOXO3, MEG3 and other tumor suppressors coincided with c-Rel nuclear expression, as well as the complicated relationships between NF-κB members and their overlapping function. However, c-Rel nuclear expression correlated with significantly poorer survival in p63+ and BCL-2− activated B-cell-like-DLBCL, and in DLBCL patients with TP53 mutations. Multivariate analysis indicated that after adjusting clinical parameters, c-Rel positivity was a significantly adverse prognostic factor in DLBCL patients with wild type TP53. Gene expression profiling suggested dysregulations of cell cycle, metabolism, adhesion, and migration associated with c-Rel activation. In contrast, REL amplification did not correlate with c-Rel nuclear expression and patient survival, likely due to co-amplification of genes that negatively regulate NF-κB activation. These insights into the expression, prognostic impact, regulation and function of c-Rel as well as its crosstalk with the p53 pathway underscore the importance of c-Rel and have significant therapeutic implications.

Details

Language :
English
Database :
OpenAIRE
Accession number :
edsair.doi...........e1e10d639b290a90ebe82e3403fe7545
Full Text :
https://doi.org/10.17615/n5x0-dx74