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Giant, symptomatic mixed vascular malformation containing a cavernoma, developmental venous anomaly, and capillary telangiectasia in a 19-month-old infant
- Source :
- Child's Nervous System. 38:1005-1009
- Publication Year :
- 2021
- Publisher :
- Springer Science and Business Media LLC, 2021.
-
Abstract
- Intracranial mixed vascular malformations (MVMs) are defined as any combination of a developmental venous anomaly (DVA), cerebral cavernous malformation (CCM), capillary telangiectasia (CTG), or arteriovenous malformation (AVM) within a single, contiguous lesion. However, most MVMs described in the literature contain only 2 pathologically discrete malformations; juxtaposition of 3 or more abnormalities in a single lesion remains exceedingly rare. We present the case of a 19-month-old female with new onset focal seizures and a 4-cm right basal ganglia lesion initially believed to be an embryonal neoplasm. She subsequently underwent gross total resection (GTR) of the lesion via a transsylvian-transinsular approach. Intraoperatively, the lesion appeared to be heterogenous and highly vascular, with areas of purplish-gray friable tissue. Pathology confirmed the lesion to be a MVM containing a CCM, CTG, and a DVA. This appears to be the first reported case of such a lesion confirmed on pathology in the literature.
- Subjects :
- medicine.medical_specialty
Pathology
business.industry
Arteriovenous malformation
General Medicine
medicine.disease
New onset
Lesion
Mixed vascular malformation
Developmental venous anomaly
Capillary telangiectasia
Pediatrics, Perinatology and Child Health
medicine
Neurology (clinical)
Neurosurgery
medicine.symptom
Embryonal neoplasm
business
Subjects
Details
- ISSN :
- 14330350 and 02567040
- Volume :
- 38
- Database :
- OpenAIRE
- Journal :
- Child's Nervous System
- Accession number :
- edsair.doi...........65371a0be634fcdd3c97857bab636cb9