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A CASE OF LYMPHANGIOLEIOMYOMATOSIS WITH MULTIPLE ANGIOMYOLIPOMAS IN THE KIDNEYS: A CASE REPORT
- Source :
- Journal of Health and Translational Medicine. 9:35-38
- Publication Year :
- 2006
- Publisher :
- Univ. of Malaya, 2006.
-
Abstract
- Lymphangioleiomyomatosis (LAM) is a rare disease. The reported prevalence is around one per million in the West but the exact prevalence in Asia is unknown. It affects primarily young women of reproductive age, with a mean age of onset at 34 years. The disease is characterised by an abnormal proliferation of smooth muscle-like cells that grow over a course of time to obstruct airways, lymphatic andblood vessels. We report a case of LAM in a young woman who presented with a spontaneous pneumothorax. Computed tomography scan of the thorax and abdomen showed homogenous thin-walled cystic lesions with normal intervening lung parenchyma and multiple lesions in her kidneys with Hounsfield units similar to that of fat.
Details
- ISSN :
- 2289392X
- Volume :
- 9
- Database :
- OpenAIRE
- Journal :
- Journal of Health and Translational Medicine
- Accession number :
- edsair.doi...........533936e4157f5a1ba90359dc70f86a87