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A Case of POEMS Syndrome Previously Diagnosed with Extramedullary Plasmacytoma
- Source :
- Korean Journal of Neuromuscular Disorders. 13:59-63
- Publication Year :
- 2021
- Publisher :
- Korean Society of Neuromuscular Disorders, 2021.
-
Abstract
- POEMS (polyneuropathy, organomegaly, endocrinopathy, monoclonal gammopathy and skin changes) syndrome is a rare multisystem disorder associated with osteosclerotic myeloma. It is characterized by peripheral polyneuropathy, presence of monoclonal plasma cell proliferative disorder, and one or more of the following features – sclerotic bone lesions, Castleman disease, elevated levels of vascular endothelial growth factor, organomegaly, extravascular volume overload, endocrinopathy, skin changes, papilledema, and thrombocytosis. Extramedullary plasmacytoma (EMP) is a rare plasma cell neoplasm that arises in isolated tissues without bone marrow involvement or systemic characteristics of multiple myeloma. Herein, we report a male patient who was previously diagnosed with EMP and later developed POEMS.
- Subjects :
- hemic and lymphatic diseases
Subjects
Details
- ISSN :
- 27652246 and 20933312
- Volume :
- 13
- Database :
- OpenAIRE
- Journal :
- Korean Journal of Neuromuscular Disorders
- Accession number :
- edsair.doi...........22cda86abf20f6a2a1cb877ea9f689da