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Pseudoxanthoma Elasticum-Like Disorder with Multiple Coagulation Factor Deficiency in a Patient with Crohn’s Disease
Pseudoxanthoma Elasticum-Like Disorder with Multiple Coagulation Factor Deficiency in a Patient with Crohn’s Disease
- Source :
- The Korean Journal of Medicine. 89:474-477
- Publication Year :
- 2015
- Publisher :
- Korean Association of Internal Medicine, 2015.
-
Abstract
- Pseudoxanthoma elasticum (PXE)-like disorder with multiple coagulation factor deficiency is a genetic disease characterized by dystrophic mineralization of the connective tissue in multiple organs such as the skin, arteries, and retina. Patients with this disorder have excessive folding and sagging of the skin with loss of recoil, as well as coagulopathy. Crohn’s disease is a chronic inflammatory condition of the gastrointestinal tract, which primary affects the small intestine, often leading to malnutrition. Here, we describe the case of a 25-year-old woman who presented with these diseases. We found that nutrient deficiency due to long-term Crohn’s disease aggravated the coagulopathy associated with PXE-like disorder. (Korean J Med 2015;89:474-477)
Details
- ISSN :
- 22890769 and 17389364
- Volume :
- 89
- Database :
- OpenAIRE
- Journal :
- The Korean Journal of Medicine
- Accession number :
- edsair.doi...........12ebf3a9d08774c000e911293d479bed
- Full Text :
- https://doi.org/10.3904/kjm.2015.89.4.474