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Familial case of oral white sponge nevus - a rare hereditary condition

Authors :
Martins Filho, Paulo Ricardo Saquete
Brasileiro, Bernardo Ferreira
Piva, Marta Rabello
Trento, Cléverson Luciano
Santos, Thiago de Santana
Source :
Repositório Institucional da UFS, Universidade Federal de Sergipe (UFS), instacron:UFS
Publication Year :
2011
Publisher :
Sociedade Brasileira de Dermatologia, 2011.

Abstract

White sponge nevus (WSN) is an autosomal dominant skin disorder characterized by white, corrugated and diffuse plaques mainly affecting the oral mucosa. The condition has a high penetrance and variable expressivity, but familial reports are uncommon. This report presents a familial case of WSN in which two sisters are affected by the disorder.

Details

Language :
English
Database :
OpenAIRE
Journal :
Repositório Institucional da UFS, Universidade Federal de Sergipe (UFS), instacron:UFS
Accession number :
edsair.dedup.wf.001..652ecfe860f9b841944d2cf24d3cb8a9