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Missense variants in RPH3Acause defects in excitatory synaptic function and are associated with a clinically variable neurodevelopmental disorder

Authors :
Pavinato, Lisa
Stanic, Jennifer
Barzasi, Marta
Gurgone, Antonia
Chiantia, Giuseppe
Cipriani, Valentina
Eberini, Ivano
Palazzolo, Luca
Di Luca, Monica
Costa, Alex
Marcantoni, Andrea
Biamino, Elisa
Spada, Marco
Hiatt, Susan M.
Kelley, Whitley V.
Vestito, Letizia
Sisodiya, Sanjay M.
Efthymiou, Stephanie
Chand, Prem
Kaiyrzhanov, Rauan
Bruselles, Alessandro
Cardaropoli, Simona
Tartaglia, Marco
De Rubeis, Silvia
Buxbaum, Joseph D.
Smedley, Damian
Ferrero, Giovanni Battista
Giustetto, Maurizio
Gardoni, Fabrizio
Brusco, Alfredo
Source :
Genetics in Medicine; November 2023, Vol. 25 Issue: 11
Publication Year :
2023

Abstract

RPH3Aencodes a protein involved in the stabilization of GluN2A subunit of N-methyl-D-aspartate (NMDA)-type glutamate receptors at the cell surface, forming a complex essential for synaptic plasticity and cognition. We investigated the effect of variants in RPH3Ain patients with neurodevelopmental disorders.

Details

Language :
English
ISSN :
10983600 and 15300366
Volume :
25
Issue :
11
Database :
Supplemental Index
Journal :
Genetics in Medicine
Publication Type :
Periodical
Accession number :
ejs63439741
Full Text :
https://doi.org/10.1016/j.gim.2023.100922