Back to Search
Start Over
Multimodality treatment of a massive cervicothoracic lymphatic-venous malformation in a 13-year-old boy
- Source :
- Journal of Pediatric Surgery Case Reports; June 2017, Vol. 21 Issue: 1 p15-18, 4p
- Publication Year :
- 2017
-
Abstract
- We report the multi-modality treatment of a massive cervicothoracic lymphatic-venous malformation (LVM) in a 13-year-old boy that was present at birth as a small cervical mass. At four years of age, sclerotherapy significantly reduced the size of the malformation but over subsequent years the mass increased dramatically in size and resulted in a consumptive coagulopathy and limited left shoulder function. Treatment with sildenafil was without effect. The consumptive coagulopathy improved with subcutaneous enoxaparin. A multi-disciplinary team excised part of the mass when he was 11 years old. After surgery, gradual enlargement of the mass and rise in d-dimer prompted treatment with sirolimus. Two sessions of sclerotherapy arrested enlargement of the mass. Multi-modality treatment resulted in a marked reduction of the LVM in the child. However, enlargement of the mass and further treatment is anticipated as a cure has not yet been found.
Details
- Language :
- English
- ISSN :
- 22135766
- Volume :
- 21
- Issue :
- 1
- Database :
- Supplemental Index
- Journal :
- Journal of Pediatric Surgery Case Reports
- Publication Type :
- Periodical
- Accession number :
- ejs41616434
- Full Text :
- https://doi.org/10.1016/j.epsc.2017.03.011