Back to Search Start Over

Adrenoleukodystrophy: a clinical variant presenting as olivopontocerebellar atrophy

Authors :
Ohno, T.
Tsuchida, H.
Fukuhara, N.
Yuasa, T.
Harayama, H.
Tsuji, S.
Miyatake, T.
Source :
Journal of Neurology; October 1984, Vol. 231 Issue: 4 p167-169, 3p
Publication Year :
1984

Abstract

A case of adrenoleukodystrophy showing neurological features of olivopontocerebellar atrophy is described. A CT scan demonstrated marked atrophy in both cerebellum and pons. ACTH stimulation produced no rise in the plasma cortisol level but a significant rise in the plasma aldosterone level. The ratios of C26:0 to C22:0 in fatty acids of sphingomyelin from erythrocyte membrane and plasma were increased.

Details

Language :
English
ISSN :
03405354 and 14321459
Volume :
231
Issue :
4
Database :
Supplemental Index
Journal :
Journal of Neurology
Publication Type :
Periodical
Accession number :
ejs16040405
Full Text :
https://doi.org/10.1007/BF00313932