Lymphangiomatosis of spleen, fallopian tube and abdominal wall associated with mucinous cystadenoma of the right ovary.

Lymphangiomas are benign tumors that results from congenital malformation of lymphatic vessels. They are generally found in the neck and axilla. When they involve multiple locations, they present as lymphangiomatosis syndrome. Generalized lymphangiomatosis associated with mucinous cystadenoma of the ovary is a very rare condition. This study describes a 13-year-old girl with lymphangiomatosis of spleen, right fallopian tube and abdominal wall associated with mucinous cystadenoma of the right ovary. Contrast-enhanced abdominopelvic computed tomography scan and magnetic resonance image showed a multiple cystic splenic mass and huge abdominopelvic cystic mass. Splenectomy, excision of right ovary and fallopian tube mass, and excision of abdominal wall mass were performed without any complications. • Lymphangiomas are benign tumors that results from congenital malformation of the lymphatic vessels. • The treatment of choice for large or symptomatic splenic lymphangiomas is complete surgical resection. • Although splenic lymphangiomas are very rare, they should be considered in the differential diagnosis of splenic tumors. [ABSTRACT FROM AUTHOR]