Characterization of Connective Tissue Disease-Associated Pulmonary Arterial Hypertension From REVEAL.

The article presents the conducted study to analyze the clinical features of patients with connective tissue disease-associated pulmonary arterial hypertension (PAH). The Registry to Evaluate Early and Long-term Pulmonary Arterial Hypertension Disease Management (REVEAL) was used in the analysis. It claims that PAH is a common complication of patients with connective tissue diseases (CTD), which specifically affects patients with systemic sclerosis (SSc), systemic lupus erythematosus (SLE) and mixed CTD (MCTD).