Atypical presentation of forearm compartment syndrome in a case of vascular type Ehlers–Danlos syndrome.

A 30-year-old Chinese man with vascular type Ehlers–Danlos Syndrome presents with spontaneous right forearm compartment syndrome due to pseudoaneurysms along the radial artery. Emergency fasciotomy and reconstruction of the radial artery with a saphenous vein graft were performed. Genetic test showed a heterozygous DNA change c. 1852 G > C in COL3A1 gene. [ABSTRACT FROM AUTHOR]