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Hereditary Hemorrhagic Telangiectasia with Diffuse Bronchopulmonary Arteriovenous Malformations.

Authors :
Masayuki Nakajima
Yuko Morishima
Kensaku Mori
Kazufumi Yoshida
Kenya Kuramoto
Masashi Matsuyama
Takumi Kiwamoto
Yosuke Matsuno
Nobuyuki Hizawa
Source :
American Journal of Respiratory & Critical Care Medicine; 9/15/2023, Vol. 208 Issue 6, p726-727, 2p
Publication Year :
2023

Abstract

The article presents a case study of a Hereditary Hemorrhagic Telangiectasia (HHT) type 2 with unique diffuse bronchopulmonary arteriovenous malformations (AVMs) that directly communicate between bronchial arteries and pulmonary veins. It discusses the diagnosis and management of this unusual presentation of HHT, emphasizing the central and diffuse nature of the AVMs and their potential impact on pulmonary circulation.

Details

Language :
English
ISSN :
1073449X
Volume :
208
Issue :
6
Database :
Complementary Index
Journal :
American Journal of Respiratory & Critical Care Medicine
Publication Type :
Academic Journal
Accession number :
172006994
Full Text :
https://doi.org/10.1164/rccm.202301-0062IM