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Hereditary Hemorrhagic Telangiectasia with Diffuse Bronchopulmonary Arteriovenous Malformations.
- Source :
- American Journal of Respiratory & Critical Care Medicine; 9/15/2023, Vol. 208 Issue 6, p726-727, 2p
- Publication Year :
- 2023
-
Abstract
- The article presents a case study of a Hereditary Hemorrhagic Telangiectasia (HHT) type 2 with unique diffuse bronchopulmonary arteriovenous malformations (AVMs) that directly communicate between bronchial arteries and pulmonary veins. It discusses the diagnosis and management of this unusual presentation of HHT, emphasizing the central and diffuse nature of the AVMs and their potential impact on pulmonary circulation.
Details
- Language :
- English
- ISSN :
- 1073449X
- Volume :
- 208
- Issue :
- 6
- Database :
- Complementary Index
- Journal :
- American Journal of Respiratory & Critical Care Medicine
- Publication Type :
- Academic Journal
- Accession number :
- 172006994
- Full Text :
- https://doi.org/10.1164/rccm.202301-0062IM